Examples of 'cystathionine' in a sentence
Meaning of "cystathionine"
cystathionine (adjective) - Cystathionine is a term used in biochemistry to describe a compound or substance related to the amino acid metabolism
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- An intermediate, 2-amino-4-(2-amino-2-carboxy-ethyl) thio-butanoic acid, in the biosynthesis of cysteine.
How to use "cystathionine" in a sentence
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cystathionine
An excess of cystathionine in the urine is called cystathioninuria.
It is necessary for the conversion of homocysteine to cystathionine.
Cystathionine is an intermediate in the synthesis of cysteine.
It results from the lysis of cystathionine.
Having a cystathionine gamma synthase activity which is inactivated.
Neither of the mutated enzymes exhibited activity towards cystathionine.
Cystathionine beta synthase deficiency.
The two recombinant enzymes were unable to utilise cystathionine as a substrate.
A weakened or inactivated cystathionine gamma synthase based on a wild type strain.
Homocystinuria is a rare inherited disorder due to a deficiency in cystathionine beta synthase.
A reduced or inactivated cystathionine gamma synthase activity based on that of a wild type protein.
The product of these transformations is lanthionine or cystathionine ketimine, respectively.
In some embodiments the cystathionine is a delta-cystathionine or a gamma-cystathionine.
These mutations disrupt the normal function of cystathionine beta-synthase.
The gene coding for cystathionine gamma-lyase activity can be deleted, if required.
See also
Classical homocystinuria is due to a deficiency in cystathionine beta synthase ( CBS ).
The enzyme cystathionine gamma-lyase converts the cystathionine into cysteine and alpha-ketobutyrate.
Homocystinuria due to cystathionine beta-synthase.
Cystathionine beta-synthase then combines homocysteine and serine to form the asymmetrical thioether cystathionine.
The transsulfuration pathway goes through cystathionine as an intermediate and utilizes cysteine as a sulfur donor.
Cystathionine Y-synthase peptide sequences are publicly available.
In some embodiments, a cystathionine is formed.
Homocystinuria due to cystathionine beta-synthase deficiency - the effects of betaine treatment in pyridoxine-responsive patients.
Transsulfuration activity, An activity that produces methionine or SAMe vía the intermediate, cystathionine.
The gas is produced from cysteine by the enzymes cystathionine beta-synthase and cystathionine gamma-lyase.
Cystathionine B-lyase peptide sequences are publicly available.
Transsulfuration - Homocysteine is converted to cystathionine by cystathionine β-synthase, before conversion to cysteine.
Cystathionine gamma-synthase catalyzes the conversion of O-succinylhomoserine to cystathionine.
It is responsible for - using vitamin B6 to convert homocysteine and serine to a molecule called cystathionine.
Genes encoding cystathionine Y-synthase peptides are also referred to herein as metB.
Transsulfuration activity, An activity that produces methionine or SAMe via the intermediate, cystathionine.
Genes encoding cystathionine B-lease peptides are also referred to herein as metC.
After the MetB reaction, cysteine turns to cystathionine which can not bind to DTNB.
Genes encoding cystathionine B-lyase peptides are also referred to herein as metC.
Condensing homocysteine in the sample using serine and an enzyme cystathionine B-synthase to form cystathionine ;.
Cystathionine beta lyase encoded by metC gene converts cystathionine into L-homocysteine.
In another embodiment, the cystathionine is a delta-cystathionine.
The PLP-dependent enzyme may be methioninase, tyrosine phenol-lyase, tyrosine aminotransferase or cystathionine beta-synthase.
In one embodiment, the cystathionine is a gamma-cystathionine.
Adjunctive treatment of homocystinuria, involving deficiencies or defects in, cystathionine beta-synthase CBS.
Cystathionine-Y-lyase ( CGI or cystathionase ) is an enzyme that breaks down cystathionine into cysteine and a-ketobutyrate.
The MetB enzyme reacts with OSHS and cysteine in a 1, 1 ratio and produces cystathionine.
Transsulfuration is catalyzed by cystathionine beta-sinthase, and vitamin B6 pyridoxine is the cofactor.
Introduction, classical homocystinuria ( hcu ) is a genetic disease caused by cystathionine ¿ - synthase ( c ¿ s ) deficiency.
Then, cystathionine synthase catalyzes the condensation of the L-homocysteine with L-serine to form L-cystathionine.
As shown in Table 5, cells overexpressing cystathionine B-lyase showed increased resistance to AEC.
Plasma homocysteine levels are elevated ≥ 10-fold in homozygous cystathionine beta-synthase deficiency.
Key words, homocysteine, cystathionine beta-synthase, cystathionine gamma-lyase, thyroid hormone.
Such non-specific cystathionine B-lyase peptides are, therefore, also included.
Such non-specific cystathionine Y-synthase peptides are, therefore, also included.
